Stiff-person syndrome: what is stiff-person syndrome?

STIFF'S SYNDROME.

Stiff-person syndrome: what is stiff-person syndrome?

STIFF'S SYNDROME. Singer Celine Dion has revealed she has a rare neurological condition called stiff-person syndrome, forcing her to postpone her 2023 European tour.

[Updated December 9, 2022 at 9:47 a.m.] Canadian singer Celine Dion revealed on Thursday, December 8, to have a rare neurological disease called "stiff-Person Syndrome" or Stiff-Person Syndrome in English, in a video posted on his Instagram account. "I was diagnosed with a very rare neurological disorder. (…) We don't know everything about this disease yet, but we now know that it is the cause of the muscle spasms I suffer from," she said. , also announcing the postponement of her European tour scheduled for 2023. This neurological pathology affects "about one in a million people", according to the singer.

This rare neurological disease mainly affects the trunk muscles, causing spasms, chronic pain and reduced mobility, including the inability to walk. "These spasms affect my everyday life at all levels. I sometimes have difficulty walking and I can't always use my vocal cords to sing as I would like," said the interpreter of I will go where you will go.

Discovered in the 1950s, this syndrome is characterized by muscle rigidity and increased sensitivity to external stresses, such as noise. Often misdiagnosed because it is confused with other diseases, Stiff-person Syndrome affects twice as many women as men and the peak incidence is around the age of 45, explains Orpha.net, "the disease portal rare." “The progressive muscular stiffness leads to immobility of the trunk and hips and the gait becomes stiff and particular”, is it detailed on the same site. For now, scientific research has not identified the causes of this disease, which would be an autoimmune reaction of the brain and spinal cord. Some painkillers can reduce the symptoms of the disease, but they do not cure it.

In her video posted on Instagram on Thursday, December 8, singer Céline Dion explains the symptoms of stiff person syndrome in her home. "I've had health problems for a long time and it's not easy for me to deal with them. Recently I was diagnosed with a very rare neurological disorder called Stiff-person syndrome, which affects approximately one in a million people. We don't yet know everything about this rare disease, but we now know that it is the cause of the muscle spasms I suffer from."

And to detail, concerning his daily life with the disease: "Unfortunately these spasms affect my everyday life, on several levels. I sometimes have a lot of difficulty walking and I cannot use my vocal cords as I would like. "

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